PEM Source

Your source for all things Pediatric Emergency Medicine

1

Question: Cardiology

(Click the link to comment and to vote – voting not working through email, sorry!)

Which of the following syndromes is associated with an increased risk of aortic dissection?
CardiologySyndrome

pemsou5_wp • April 7, 2020


Previous Post

Next Post

Comments

  1. Kelly April 8, 2020 - 9:54 pm Reply

    E) All of the above
    Connective tissue disorders such as Marfan syndrome and Ehlers-Danlos as well as other syndromes that lead to cystic medial necrosis of the proximal aorta predispose patients to aortic dissection. Other syndromes include: Turner, Noonan, homocystinuria, osteogenesis imperfecta, and Loeys-Dietz syndrome. Aortic dissections classically present as acute onset of severe chest or back pain, often described as “ripping” or “tearing” pain. Patients may have a pulse deficit and/or > 20 mm Hg variation in SBP between arms.

Leave a Reply

Your email address will not be published / Required fields are marked *