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Question: Cardiology

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Which of the following syndromes is associated with an increased risk of aortic dissection?

pemsou5_wp • April 7, 2020

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  1. Kelly April 8, 2020 - 9:54 pm Reply

    E) All of the above
    Connective tissue disorders such as Marfan syndrome and Ehlers-Danlos as well as other syndromes that lead to cystic medial necrosis of the proximal aorta predispose patients to aortic dissection. Other syndromes include: Turner, Noonan, homocystinuria, osteogenesis imperfecta, and Loeys-Dietz syndrome. Aortic dissections classically present as acute onset of severe chest or back pain, often described as “ripping” or “tearing” pain. Patients may have a pulse deficit and/or > 20 mm Hg variation in SBP between arms.

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